Low serum haptoglobin and blood films suggest intravascular haemolysis contributes to severe anaemia in hereditary haemorrhagic telangiectasia.

HAEMATOLOGICA(2019)

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摘要
Hereditary hemorrhagic telangiectasia (HHT) results in iron deficiency anemia due to chronic blood losses from telangiectasia and arteriovenous malformations in the nose and gastrointestinal tract. Patients with HHT can require very frequent intravenous iron infusions or blood transfusions in
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关键词
Red Cells,anaemia,hereditary haemorrhagic telangiectasia
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