Anaesthetic management of uncorrected Tetralogy of Fallot and mitochondrial disorder: a role for Dexmedetomidine.

The case presented is a patient with uncorrected cyanotic congenital heart disease (CHD) and a mitochondrial disorder, and highlights the need for understanding of the physiological sequelae and impact of anaesthesia for these disorders. A 9-year-old boy with uncorrected Tetralogy of Fallot (TOF) and mitochondrial disorder presented for palliative right ventricular outflow tract (RVOT) stent insertion. Given the severity of his developmental delay and guarded prognosis, definitive surgical management was not undertaken earlier in life. This article is protected by copyright. All rights reserved.