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Paroxysmal sympathetic hyperactivity following status epilepticus in a 22-year-old with Juvenile Neuronal Ceroid Lipofuscinosis: A case report

Molly D. Himmelrich, Jennifer M. Pritchard,Camilo Gutierrez,Tara L. M. Dutta

Epilepsy & Behavior Reports(2021)

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摘要
•Late sequalae of juvenile neuronal ceroid lipofuscinosis are seen in older patients.•Status epilepticus may incite paroxysmal sympathetic hyperactivity in JNCL.•PSH may be clinically confused with seizures in JNCL complicated by epilepsy.•PSH can be found in a patient with JNCL without infection or inciting factors.
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关键词
Paroxysmal sympathetic hyperactivity,Juvenile neuronal ceroid lipofuscinosis,Batten disease,Status epilepticus,Seizure,Case report
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