Thoracic Giant Nervous Tumor During The Von Recklinghausen Disease
REVUE DE PNEUMOLOGIE CLINIQUE(2014)
摘要
We report the case of a patient aged 23, admitted for bilateral intrathoracic tumor, including a giant right. Surgery was performed by right sternothoracotomy. After 7 days, she presented an irreversible cardiac arrest. The malignant peripheral nerve sheath tumors are rare and aggressive. Their incidence is 0.001% in the general population and 0.16% in patients with neurofibromatosis type 1. These tumors are characterized by their risk of recurrence and poor prognosis. The treatment is the surgical resection. We analyze incidence, diagnosis and prognosis of these tumors. (C) 2013 Elsevier Masson SAS. All rights reserved.
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关键词
Malignant peripheral nerve sheath, Neurofibromatosis type I, Giant intrathoracic tumors
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