Linear childhood discoid lupus erythematosus along a Blaschko's line of the arm

Linear childhood discoid lupus erythematosus (DLE) is a rare variant of DLE with a linear distribution that preferentially occurs on the face and scalp of children. We report a rare case of linear childhood DLE on the Blaschko's line of his left upper arm of a 7-year-old Japanese boy with 4-year history of the disease. He was positive for anti-single-stranded DNA antibodies, but still showed no systemic symptoms during the 3-year follow-up period. We reviewed previous reports on linear childhood DLE and found that patients with nonfacial/nonscalp skin lesions are significantly more likely to be positive for autoantibodies.