Late-Onset Status Epilepticus Associated With Isolated Leptomeningeal Angioma and Sturge-Weber Syndrome-Related GNA11 Pathogenic Variation.

A 61-year-old man with no neurologic history presented with 2 episodes of super-refractory left-sided focal motor status epilepticus 5 months apart. He developed a prolonged postictal left hemiparesis each time that improved over several weeks. He also experienced recurrent and transient left hemiplegia independently of any seizure after hypovolemic and septic shocks.