Forme Pseudo-Pathomimique De Granulomatose Avec Polyangéite (anciennement Maladie De Wegener)

Introduction. - ANCA vasculitis may involve the skin and develop slowly without specific histology, and without autoantibodies.Case report. - We report a 50-year-old woman who experienced bilateral mastectomy because of ulceronecrotic, non-specific inflammatory cutaneous lesions of the breasts. First considered by others as a malinger patient, she developed oto-neurological lesions leading to the diagnosis of Wegener's granulomatosis. Five years later, specific antibodies of the disease were present.Conclusion. - Cutaneous involvement by ANCA vasculitis can be isolated for a long time. Physicians must have a high degree of suspicion to avoid diagnostic delay of ANCA vasculitis. (C) 2013 Societe nationale francaise de medecine interne (SNFMI). Published by Elsevier Masson SAS. All rights reserved.