1st Italian SMA Family Association Consensus Meeting:

•This paper reviews and updates recommendations for respiratory care stratified by disease type and severity.•Specifically the paper describes the management pathway in SMA I at diagnosis and at follow-up.•Respiratory assessment and follow-up recommendations in SMA II and IIIA.•Criteria for NIV launching in SMA II and IIIA.•Secretion management protocols in SMA II and III.