Congenital Partial Arhinia: A Rare Malformation Of The Nose Coexisting With Intracranial Arachnoid Cyst

Arhinia is the congenital partial or complete absence of the soft tissue of the nose and nasal structures. It is an extremely rare defect of embryogenesis and is generally associated with other craniofacial anomalies like arachnoid cysts and also midline defects such as cleft palate, absence of paranasal sinuses, and other palatal and ocular abnormalities. Less than 40 patients with arhinia have been reported so far in the history of modern medicine. We report herein a patient with congenital partial arhinia with intracranial arachnoid cyst and discuss the embryology and review of literature of such a rare disease