Progressive diffuse meningioangiomatosis: Response to bevacizumab treatment.

Meningioangiomatosis is an uncommon nonmalignant disorder characterized by a progressive focal lesion, typically presenting as seizure disorder.(1) Histologically, the lesion exhibits prominent cortical vasculature with associated perivascular mesenchymal cell proliferation. The standard treatment is surgical resection.(1,2) Here we describe a patient with diffuse meningioangiomatosis that caused permanent cortical blindness. He was treated with bevacizumab with resultant clinical stabilization and marked radiographic improvement.