Dual diagnosis of Histiocytoid Sweet Syndrome and ANCA-vasculitis, a case report

Histiocytoid Sweet syndrome (H-SS) is a rare variant of acute febrile neutrophilic dermatosis. It is frequently associated with hematologic malignancies but has also been associated with certain inflammatory states. Here we report a case of concurrent anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis and H-SS diagnoses.