A Case of Lymphangioleiomyomatosis with Endometrial Cancer Diagnosed by Retroperitoneoscopic Para-Aortic Lymph Node Dissection

Lymphangioleiomyomatosis (LAM) is a rare disease in which multiple cysts are formed mainly in the lungs and symptoms such as dyspnea, bloody sputum, and chyle effusion appear. We experienced a case of endometrial cancer with a para-aortic mass that was initially suspected to be due to metastasis. However, after resection by retroperitoneoscopic surgery, the mass was diagnosed as LAM and fertility-sparing therapy was started.