A novel association of osmotic demyelination in Sjögren's syndrome prompts revisiting role of aquaporins in CNS demyelinating diseases: A literature review

Multiple Sclerosis and Related Disorders(2023)

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摘要
•Novel association of osmotic demyelination syndrome in Sjögren's syndrome.•Osmotic demyelination, not neuromyelitis optica spectrum disorder associated with renal tubular acidosis.•Osmotic demyelination syndrome in Sjögren's associated with hypokalaemia and/or hypernatremia but not hyponatremia.•Aquaporin defects may be implicated in the pathogenesis of osmotic demyelination syndrome in Sjögren's syndrome.
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关键词
Central pontine myelinolysis,Sjogren's syndrome,renal tubular acidosis,neuromyelitis optica spectrum disorders,Aquaporin,hypokalemia
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