Surgical exposure of teeth in cleidocranical dysplasia under procedural sedation:- case report

Tamanna Bhagat, Harsimran Kaur, Supriya Deswal,Satya Narain,Hemant Batra

PARIPEX INDIAN JOURNAL OF RESEARCH(2023)

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摘要
Cleidocranial Dysplasia (CCD) is a rare autosomal dominant condition which is mainly characterised by skeletal abnormalties like hypoplastic or aplastic clavicles, increase in transverse diameter of the cranium, delayed closure of fontanelles with presence of open sutures and skeletal changes in maxilla and mandible. 2,4 These patients usually presents with delayed exfoliation of deciduous teeth, delayed or failed eruption of the permanent dentition with multiple supernumerary teeth, protruding mandible and mid- face retrusion.2 We present a case report of a 16 year old girl undergoing multiple surgical exposure of impacted permanent teeth under conscious sedation so as to move them in normal occlusion with orthodontic traction
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关键词
cleidocranical dysplasia,teeth,surgical exposure
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