OBJECTIVE:We report a case of laparoscopic nephrectomy of a cross-fused ectopic kidney in a 4-year-old girl with renal hypertension and Fanconi anemia.MATERIALS AND METHODS:We performed a transperitoneal laparoscopy. Ectopic kidney resection was done after dissection of the pathological kidney and after clamping vessels, using an ultrasonic device. Hospitalization time was 4 days.RESULTS:At 6 months, blood pressure was normalized and the patient showed an adequate growth curve.CONCLUSION:The transperitoneal route is very effective when a nephrectomy is necessary. It offers perfect exposure with limited risk of complications.