We report an observation of an uncommon form of extra-papillary myelin fibers of fortuitous discovery in a patient, 55 years old, who consulted for a change of correction. The clinical aspect of the fundus led to the diagnosis of retinal myelin fibers in front of a whitish placard with a finely striated scalloped edge, partially masking the vessels and located at the level of the inferior temporal arch. These fibers, contiguous to the papilla or distant from it, have an incidence varying from 0.57% to 0.98% according to studies and their pathogenesis is still uncertain. This congenital anomaly of the retinal fibers of clinical diagnosis is often asymptomatic, but can however be associated with other ocular disorders.
Bests disease is an autosomal dominant hereditary macular dystrophy characterized by the presence of auto-fluorescent vitelline deposits. We report a case of a vitelliform stage of bests disease in a 23-year-old female patient. The diagnosis was made based on the fundus appearance: egg yolk macular lesion, hypofluorescence in the early stages, OCT appearance and alteration of the electro-oculogram and the electroretinogram. The exact frequency of this condition is difficult to determine and varies according to the various studies. It is thought to account for 4% of all retinal dystrophies. Its management is an annual surveillance.
La rougeole est une pathologie virale du sujet jeune liée à une infection par un paramyxovirus. La rougeole systémique passe par quatre phases : incubation, invasion, éruption et desquamation. C’est une maladie essentiellement bénigne du point de vue oculaire dans son stade initial, les lésions sont souvent cornéennes, pouvant évoluer vers des complications telles que le leucome adhérent. Nous rapportons un cas de leucome adhérent bilatéral et asymétrique secondaire à une atteinte oculaire de la rougeole à l’enfance.
Pigmentary retinopathy refers to a group of inherited degenerative diseases of the retina, which primarily affects the photoreceptor cells in the retina. The association with congenital hearing loss defines Usher syndrome. Usher syndrome is a rare pathology of autosomal recessive transmission with a double sensory impairment (auditory and visual). We report the observation of a 12-year-old patient from a consanguineous marriage with congenital deafness, normal vestibular function and pigmentary retinopathy composing type 2 of Usher syndrome.
Orbital metastases are a rare disease entity compared to choroidal metastases, and they are only rarely the first of a primary cancer. The primary tumor is often breast cancer, prostate cancer and then lung cancer. Orbital metastases generally induce an isolated exophthalmos, which appears rapidly. Orbito-cerebral MRI is the imaging method of choice for the diagnosis of orbital metastases. But a fine needle biopsy of the orbital mass is the most reliable method to confirm the diagnosis. Unfortunately, the vital prognosis is poor and the treatment will be palliative. We report the case of a 67-year-old male patient, chronically smoking, who presented with an inaugural orbital metatasis from pulmonary adenocarcinoma. Ocular metastasis was revealed in our patient by exophthalmos associated with reduced visual acuity. Unfortunately, the patient died after a few weeks, testifying to the poor prognosis of these orbital metastases.
Diabetic macular edema (DME) is a thickening of the macular retina secondary to a rupture of the internal blood-retinal barrier. It is the leading cause of low vision in diabetic patients.[1] The functional prognosis depends on several anatomical factors. The spectral domain optical coherence tomography (SD-OCT) is an important tool for the diagnosis, therapeutic indication and monitoring of diabetic macular edema.