Objective: To study the epidemiological features of Adult Congenital Biliary Dilatation and its diagnosis and treatment.Methods: Reports on adult congenital biliary dilatation published from 1990 to 2010 were retrieved from various databases,such as China National Knowledge Infrastructure(CNKI),VIP.The epidemiological features of adult congenital biliary dilatation and its diagnosis and treatment were analyzed.Results: A total of 5146 patients with adult congenital bil-iary dilatation were reported in China during the last 21 years.The average ages and accurate ages were reported in 4298 cases,the average age of them was 34.84 years,male and female ratio is about 1:2.55,43.44% of the cases were located in East China,68.38% of the patients had varying degrees of abdominal pain,25.22% of patients have fever or symptoms of high fever,32.46% of patients with varying degrees of jaundice,18.31% patients with palpable abdominal mass,with the typical triad of the performance of patients accounted for 15.98%.Todani type Ⅰ-type accounts for 79.81%,Ⅱ-type accounted for 4.34%,Ⅲ-type accounted for 1.17%,Ⅳ-type accounting for 11.78%,Ⅴ-type accounting for 2.48%.Surgical treatment as the main treatment,bile duct cyst excision and bile duct jejunum Roux-en-YKiss surgery,accounting for 71.63%;postoperative cholangitis symptoms,the rate was 12.24%;postoperative follow-up rate of 83.55%,the cure rate 86.84 %.Conclusion: Adult women with congenital bile duct dilatation occur,mainly in eastern China,Todani type Ⅰ-based,biliary-enteric cyst excision + Roux-en-Y anastomosis as the main procedure of treatment.

Objective: To investigate the epidemiological features,diagnosis and treatment of splenic inflammatory myofibroblastic tumor in China during the past 25 years.Methods: The clinical data of 64 patients diagnosed splenic inflammatory myofibroblastic tumor(Splenic inflammatory pseudotumor) published from 1985 to 2010 from various databases,including China National Knowledge Infrastructure(CNKI),VIP,and the epidemiological features,diagnosis and treatment of SIMT patients were retrospectively analyzed.Results: There were 64 patients,including 39 males and 25 females(1.56:1).And their age spread from 24 to 74 with an average of 49.2.Most of patients had not special symptoms,and were diagnosed through routine examinations such as type-B ultrasonic or CT scan.Epigastric pain,debilitation,low-grade fever and some other untypical symptoms might appear in some patients.A solitary splenic lesion might be seen during medical imageologcal examination.Histological types: hypocellular fibrous pattern(n=26),myxoid/vascular pattern(n=12),compact spindle cell pattern(n=5).Immunophenotypic findings show that the spindle cells were positive for Vimentin,SMA in most cases.For most patients,splenectomy were the mainly treatment,and there were no signs of relapse and metastasis after the operation.Conclusion: Splenic inflammatory myofibroblastic tumor is extremely rare in china,and there are not special clinical symptoms or signs.It can be identified by characteristics of medical imaging,histologic and immunophenotypic findings with other splenic lesions.But it is difficult to define its nature preoperatively.Splenectomy is the mainly treatment with a satisfactory prognosis.

脾脏炎性肌纤维母细胞瘤(splenic inflammatory myofibroblastic tumor,SIMT)是一种少见的脾脏肿瘤,多发于中老年人,预后良好.我院2008年1月至2011年10月共收治SIMT患者5例,现报道如下.临床资料1.一般资料:本组患者男4例,女1例.年龄30～53岁,平均40.8岁.临床表现及病史:3例查体时B超发现脾占位性病变,另外2例表现为左上腹疼痛.病程最短1d,最长3个月。