Introduction. - The vertebrae are the most common localization of hydatid disease of bone. This can lead to fatal consequences.Case report. - We report the case of a 40-year-old-man, from a rural area, who had symptoms of medullary compression. The diagnosis of primary vertebral hydatid cyst, already suspected on the imaging data, was confirmed. A right posterolateral thoracotomy allowed drainage of the cyst and relief of the medullary compression. Medical treatment with albendazole was continued for 4 months. The postoperative course was uneventful and the symptoms of medullary compression resolved progressively. No recurrence was observed during a follow-up of 24 months.Conclusion. - Vertebral localization of hydatid disease is the most common and serious skeletal complication. Thoracotomy allows drainage of the cyst and the pleural cavity, and relieves the medullary compression. (c) 2012 Published by Elsevier Masson SAS on behalf of SPLF.

The osseous exostose is a rare benign tumor of the bone from which the vascular complications can be of venous or arterial order, are translated in various boards. We report the case of a young adult who presents a forgery aneurysm of the right popliteal artery with the popliteal artery booby-trapped to the left. The patient benefited from surgical treatment with good clinical and radiological evolution.

The osseous exostose is a rare benign tumor of the bone from which the vascular complications can be of venous or arterial order, are translated in various boards. We report the case of a young adult who presents a forgery aneurysm of the right popliteal artery associated with a popliteal artery booby-trapped to the left. The patient benefited from a surgical treatment with good clinical and radiological evolution. (C) 2011 Published by Elsevier Masson SAS.

L’exostose osseuse est une tumeur bénigne rare de l’os dont les complications vasculaires peuvent être d’ordre veineux ou artériel se traduisent en différents tableaux. Nous rapportons le cas d’un jeune adulte qui présente un faux anévrisme de l’artère poplitée droite associée à une artère poplitée piégée à gauche. Le patient a bénéficié d’un traitement chirurgical avec bonne évolution clinique et radiologique.

Familial idiopathic pulmonary fibrosis (IPF) is a very rare and progressively fatal disease. Its pathogenesis is not fully understood and involves damage to alveolar epithelial cells of possibly immunological, microbiological or chemical origin, leading to fibrosing healing. A genetic predisposition has been demonstrated. The authors report the case of a female patient whose brother died at the age of 29 from IPF. She had epidermodysplasia verruciformis since childhood, with the absence of pubertal development. At the age of 31, she presented diffuse interstitial pneumonia. A lung biopsy confirmed the diagnosis of IPF. Endocrine explorations detected hypogonadotropic hypogonadism, primary hypothyroidism and magnetic resonance imaging revealed an empty sella turcica. The association of familial IPF, autoimmune polyendocrinopathy and genetic dermatosis caused by a cellular immune deficiency supports the hypothesis of an immune dysfunction in the pathogenesis of IPF. (C) 2009 Elsevier Masson SAS. All rights reserved.

Between January 1990 and December 2006. 93 patients with infective endocarditis on native valves were operated in the active phase of the disease. The average age Of our patients was 32 years, with a male ascendancy. The causal heart disorder was found in 89% of the cases, dominated by rheumatoid arthritis. The germ in cause was isolated in 52.6% of the Cases. The operative indication was hemodynamic in 29 cases, infectious in nine cases, mixed in 29 cases and embolic in 26 cases. The average operating delay was of 13 days with regard to the beginning of the antibiotic treatment. We realized a valvular aortic replacement at 32 patients with reconstruction of the ring in six cases, a valvular mitral replacement at 29 patients. a mitroaortic replacement at 21 patients, a reconstructive mitral surgery in nine cases, a valvular tricuspid replacement in one case and a reconstructive tricuspid surgery in one case. The early mortality was 13%. The follow-up Was 89% with an average recession of 3.1 years and a late mortality of 5%. The aim of this study is to analyze the immediate and late results of the surgery of infective endocarditis in the active phase and to bring to light the prognostic factors of mortality. (C) 2009 Elsevier Masson SAS. All rights reserved.

Idiopathic renal arteriovenous fistulas are extremely rare. They are believed to occur as the result of congenital renal artery aneurysm that erodes into an adjacent vein. We report a case of a 48-year-old man in whom we discovered fortuitously a painless mass of the right flank. Computed tomography revealed a huge renal artery aneurysm with giant arteriovenous fistula in the absence of any clinical stigmata. Given the size of the fistula and the partial destruction of the renal parenchyma, nephrectomy was successfully performed.

Les fistules artério-veineuses rénales idiopathiques sont extrêmement rares. Elles sont supposées être le résultat d’une érosion d’une veine rénale par un anévrysme congénital de l’artère rénale adjacente. Nous rapportons ici le cas d’un homme de 48 ans chez qui nous avons découvert fortuitement une masse douloureuse du flanc droit. Un angioscanner a révélé la présence d’un volumineux anévrysme de l’artère rénale droite avec fistule artério-veineuse géante, en l’absence de tout stigmate clinique. Etant donné la taille de la fistule et de la destruction partielle du parenchyme rénal, une néphrectomie a été décidée et réalisée avec succès.

Entre janvier 1991 et décembre 2006, 56 patients, porteurs d’un canal atrioventriculaire (CAV) partiel, ont été opérés. Le but de cette étude rétrospective est d’analyser les résultats immédiats et lointains de la chirurgie en accordant de l’importance à deux principaux problèmes qui sont les troubles du rythme et de la conduction, ainsi que l’insuffisance mitrale (IM) résiduelle. L’âge moyen de nos patients est de dix ans et demi avec une nette prédominance féminine. Quatre-vingt-treize pour cent des patients étaient en rythme régulier sinusal. Aucun cas de bloc auriculoventriculaire (BAV) complet n’a été noté. L’IM était de grade I dans 28,5 % des cas, de grade II dans 60 % des cas et de grade III et IV dans 7,5 % des cas. La fuite était minime dans 4 % des cas. La correction s’est faite sous circulation extracorporelle et a consisté en une suture de la fente mitrale dans la plupart des cas avec fermeture de l’ostium primum par un patch de péricarde. La mortalité périopératoire était de 1,8 % des cas. Les troubles du rythme et de la conduction ont été notés dans 34 % des cas. Tous les patients ont été contrôlés avec un recul moyen de six ans et sept mois. La mortalité secondaire était nulle. L’IM à moyen terme était minime dans 78 % des cas. Le CAV partiel est une cardiopathie congénitale dont l’évolution spontanée peut être grevée de complications, notamment les troubles du rythme et de la conduction, ainsi que l’insuffisance cardiaque, ce qui justifie une réparation chirurgicale précoce.

La sténose trachéale congénitale (STC) est une malformation très rare (0,3 à 1 % des sténoses laryngotrachéales) et potentiellement létale. Elle constitue également une cause rare de stridor congénital. Les auteurs rapportent une nouvelle observation de STC chez un petit nourrisson et analysent ses particularités.

BACKGROUND:Alveolar soft part sarcoma is rare; it mainly appears in the lower extremities in adults and the head and neck in children. Primary pulmonary occurrence of this tumour is exceptional.OBSERVATION:We report a new case in a 49-year-old man who presented with thoracic pain developing over one month. Imaging showed a tumour in the left upper lobe. Diagnosis of primary alveolar sarcoma of the lung was made by histological examination of a biopsy specimen and elimination of a primary soft tissue tumour elsewhere.CONCLUSION:Primary alveolar sarcoma of the lung is exceptionally rare and the diagnosis should only be made after eliminating a soft tissue tumour elsewhere.

The cardiac location of the echinococcosis is rare. It is associated with complications potentially severe. Indeed, the break inside the cardiac chambers with pulmonary embolism is the inevitable complication of the echinococcosis of the right heart. Between January 1992 and January 2006, five patients were operated in the department of cardiac surgery of Sousse (Tunisia) for an emboligenous hydatid cyst of the right heart. The average age is of 30 years with extremes from 18 to 65 years. The cardio-pulmonary bypass is the technique of choice. We regretted a single death in immediate postoperative period. All the patients were controlled with an average recession of 36 months. A single late death was noticed. No recurrence was observed.

The coronary fistula is a rare abnormality making communicate a coronary artery with a cardiac cavity or a great vessel, so bypassing the myocardial capillary network. The majority of these fistulas are congenital but can nevertheless arise after a cardiac surgery. The right coronary artery and the left anterior descending coronary artery are mostly concerned. The circumflex coronary artery is rarely involved. The most frequent site of drainage is the right ventricle. We report the case of a 2-year-old child, brought by his parents for dyspnoea of effort. The diagnosis of coronary fistula was confirmed by the coronary angiography which showed an aneurysmal circumflex artery, draining into the right ventricle. The intervention was led under cardiopulmonary bypass. We proceeded to the longitudinal opening of the aneurysm then to the blindness of the fistula. The postoperative course was simple.